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Southern, Kevin W ORCID: 0000-0001-6516-9083 (2021) Achieving respiratory excellence in pre-school children with cystic fibrosis. JOURNAL OF CYSTIC FIBROSIS, 20 (6). pp. 904-905.

O'Toole, Daniel PH, Latchford, Gary J, Duff, Alistair JA, Ball, Rosemary, McCormack, Pamela, McNamara, Paul S ORCID: 0000-0002-7055-6034, Brownlee, Keith G and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2019) Adherence to Aerosol Therapy in Young People With Cystic Fibrosis: Patient and Parent Perspectives Following Electronic Data Capture. QUALITATIVE HEALTH RESEARCH, 29 (6). pp. 846-856.

Francis, Natalie Z and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2022) Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 9 (9). CD002204-.

Patel, Tulsi Prafull Assessing the impact of administering the 'Challenges of Living with Cystic Fibrosis' questionnaire on the self-efficacy of caregivers of children with cystic fibrosis. Master of Philosophy thesis, University of Liverpool.

Aslam, Aisha A, Sinha, Ian P and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2023) Ataluren and similar compounds (specific therapies for premature termination codon class I mutations) for cystic fibrosis. The Cochrane database of systematic reviews, 3 (3). CD012040-CD012040.

McCormack, Pamela, Burnham, Paul and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2017) Autogenic drainage for airway clearance in cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 10 (10). CD009595-.

Sinha, Ian P, Harwood, Rachel ORCID: 0000-0003-3440-3142, Semple, Malcolm G ORCID: 0000-0001-9700-0418, Hawcutt, Daniel B ORCID: 0000-0002-8120-6507, Thursfield, Rebecca, Narayan, Omendra, Kenny, Simon E, Viner, Russell, Hewer, Simon Langton and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2020) COVID-19 infection in children. LANCET RESPIRATORY MEDICINE, 8 (5). pp. 446-447.

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Chudleigh, Jane, Shakespeare, Lynette, Holder, Pru, Chinnery, Holly, Hack, Gemma, Gill, Tanya, Gould, Rachel, Southern, Kevin W ORCID: 0000-0001-6516-9083, Olander, Ellinor K, Morris, Stephen et al (show 3 more authors) , Bonham, James R, Simpson, Alan and Moody, Louise (2022) Co-designing Improved Communication of Newborn Bloodspot Screening Results to Parents: Mixed Methods Study. Journal of participatory medicine, 14 (1). e33485-e33485.

Armstrong, Rachael E, Frith, Lucy ORCID: 0000-0002-8506-0699, Ulph, Fiona M and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2020) Constructing a Bioethical Framework to Evaluate and Optimise Newborn Bloodspot Screening for Cystic Fibrosis. International Journal of Neonatal Screening, 6 (2). 40-.

Armstrong, Rachael E, Frith, Lucy ORCID: 0000-0002-8506-0699, Ulph, Fiona M ORCID: 0000-0003-3590-6542 and Southern, Kevin W (2020) Constructing a Bioethical Framework to Evaluate and Optimise Newborn Bloodspot Screening for Cystic Fibrosis. International journal of neonatal screening, 6 (2).

Southern, Kevin W ORCID: 0000-0001-6516-9083, Murphy, Jared, Sinha, Ian P and Nevitt, Sarah J ORCID: 0000-0001-9988-2709 (2020) Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 12 (12). CD010966-.

Southern, Kevin W ORCID: 0000-0001-6516-9083, Patel, Sanjay, Sinha, Ian P and Nevitt, Sarah J ORCID: 0000-0001-9988-2709 (2018) Correctors (specific therapies for class II CFTR mutations) for cystic fibrosis. Cochrane Database of Systematic Reviews, 8 (8). CD010966-.

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Munck, Anne, Southern, Kevin W, Murphy, Jared ORCID: 0000-0003-4656-3004, de Winter-de Groot, Karin M, Gartner, Silvia, Karadag, Bülent, Kashirskaya, Nataliya, Linnane, Barry, Proesmans, Marijke, Sands, Dorota et al (show 4 more authors) , Sommerburg, Olaf, Castellani, Carlo, Barben, Jürg and European CF Society Neonatal Screening Working Group (ECFS NSWG), (2023) Cystic Fibrosis Cases Missed by Newborn Bloodspot Screening-Towards a Consistent Definition and Data Acquisition. International journal of neonatal screening, 9 (4). p. 65.

Ren, Clement L, Borowitz, Drucy S, Gonska, Tanja, Howenstine, Michelle S, Levy, Hara, Massie, John, Milla, Carlos, Munck, Anne and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2017) Cystic Fibrosis Transmembrane Conductance Regulator-Related Metabolic Syndrome and Cystic Fibrosis Screen Positive, Inconclusive Diagnosis. JOURNAL OF PEDIATRICS, 181. S45-+.

Barben, Jurg and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2016) Cystic fibrosis screen positive, inconclusive diagnosis. CURRENT OPINION IN PULMONARY MEDICINE, 22 (6). pp. 617-622.

Sinha, Aditi and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2021) Cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID). BREATHE, 17 (3). 210088-.

Fusco, Francesco, Chudleigh, Jane, Holder, Pru, Bonham, James R, Southern, Kevin W ORCID: 0000-0001-6516-9083, Simpson, Alan, Moody, Louise, Olander, Ellinor K, Chinnery, Holly and Morris, Stephen (2022) Delivering Positive Newborn Screening Results: Cost Analysis of Existing Practice versus Innovative, Co-Designed Strategies from the ReSPoND Study. INTERNATIONAL JOURNAL OF NEONATAL SCREENING, 8 (1). 19-.

Glasscoe, Claire ORCID: 0000-0003-1600-8202, Hope, Holly F, Lancaster, Gillian A, McCray, Gareth, West, Kiri, Patel, Latifa, Patel, Tulsi, Hill, Jonathan, Quittner, Alexandra L and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2023) Development and preliminary validation of the challenges of living with cystic fibrosis (CLCF) questionnaire: a 46-item measure of treatment burden for parent/carers of children with CF. PSYCHOLOGY & HEALTH, 38 (10). pp. 1309-1344.

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Farrell, Philip M, White, Terry B, Ren, Clement L, Hempstead, Sarah E, Accurso, Frank, Derichs, Nico, Howenstine, Michelle, McColley, Susanna A, Rock, Michael, Rosenfeld, Margaret et al (show 4 more authors) , Sermet-Gaudelus, Isabelle, Southern, Kevin W ORCID: 0000-0001-6516-9083, Marshall, Bruce C and Sosnay, Patrick R (2017) Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation. JOURNAL OF PEDIATRICS, 181. S4-S15.

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Castellani, Carlo, Duff, Alistair JA, Bell, Scott C, Heijerman, Harry GM, Munck, Anne, Ratjen, Felix, Sermet-Gaudelus, Isabelle, Southern, Kevin W ORCID: 0000-0001-6516-9083, Barben, Jurg, Flume, Patrick A et al (show 12 more authors) , Hodkova, Pavia, Kashirskaya, Nataliya, Kirszenbaum, Maya N, Madge, Sue, Oxley, Helen, Plant, Barry, Schwarzenberg, Sarah Jane, Smyth, Alan R, Taccetti, Giovanni, Wagner, Thomas OF, Wolfe, Susan P and Drevinek, Pavel (2018) ECFS best practice guidelines: the 2018 revision. JOURNAL OF CYSTIC FIBROSIS, 17 (2). pp. 153-178.

Patterson, Katie D, Walsh, Adam, McCormack, Pamela and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2019) Exercise versus airway clearance techniques for people with cystic fibrosis. Cochrane Database of Systematic Reviews, 2019 (3).

Heinz, Katie D, Walsh, Adam, Southern, Kevin W ORCID: 0000-0001-6516-9083, Johnstone, Zoe and Regan, Kate H (2022) Exercise versus airway clearance techniques for people with cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 6 (6). CD013285-.

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Allen, Lucy, Allen, Lorna, Carr, Siobhan B, Davies, Gwyneth, Downey, Damian, Egan, Marie, Forton, Julian T, Gray, Robert, Haworth, Charles, Horsley, Alexander et al (show 3 more authors) , Smyth, Alan R, Southern, Kevin W ORCID: 0000-0001-6516-9083 and Davies, Jane C (2023) Future therapies for cystic fibrosis. Nature communications, 14 (1). p. 693.

Colombo, Carla, Burgel, Pierre-Regis, Gartner, Silvia, van Koningsbruggen-Rietschel, Silke, Naehrlich, Lutz, Sermet-Gaudelus, Isabelle and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2020) Impact of COVID-19 on people with cystic fibrosis. LANCET RESPIRATORY MEDICINE, 8 (5). E35-E36.

Schlüter, Daniela K, Southern, Kevin W ORCID: 0000-0001-6516-9083, Dryden, Carol, Diggle, Peter and Taylor-Robinson, David ORCID: 0000-0002-5828-7724 (2020) Impact of newborn screening on outcomes and social inequalities in cystic fibrosis: a UK CF registry-based study. Thorax, 75 (02). pp. 123-131.

Chudleigh, Jane, Barben, Juerg, Ren, Clement L and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2022) International Approaches to Management of CFTR-Related Metabolic Syndrome/Cystic Fibrosis Screen Positive, Inconclusive Diagnosis. INTERNATIONAL JOURNAL OF NEONATAL SCREENING, 8 (1). 5-.

Skilton, Mica, Krishan, Ashma, Patel, Sanjay, Sinha, Ian P and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2019) Potentiators (specific therapies for class III and IV mutations) for cystic fibrosis. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 1 (1). pp. 1-120.

Johnson, Faye, Southern, Kevin W ORCID: 0000-0001-6516-9083 and Ulph, Fiona (2019) Psychological Impact on Parents of an Inconclusive Diagnosis Following Newborn Bloodspot Screening for Cystic Fibrosis: A Qualitative Study. INTERNATIONAL JOURNAL OF NEONATAL SCREENING, 5 (2). 23-.

Southern, Kevin W ORCID: 0000-0001-6516-9083, Barben, Jürg, Goldring, Stephen, Kneen, Rachel, Southward, Suzanne, Rajeev, Yashavi, Davies, Jane C and Bush, Andrew (2023) Raised Intracranial Pressure in Three Children with Cystic Fibrosis Receiving Elexacaftor-Tezacaftor-Ivacaftor Modulator Therapy. American journal of respiratory and critical care medicine, 208 (1). pp. 103-105.

Johnson, Faye, Ulph, Fiona, MacLeod, Rhona and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2022) Receiving results of uncertain clinical relevance from population genetic screening: systematic review & meta-synthesis of qualitative research. EUROPEAN JOURNAL OF HUMAN GENETICS, 30 (5). pp. 520-531.

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Burgel, Pierre-Régis, Southern, Kevin W ORCID: 0000-0001-6516-9083, Addy, Charlotte, Battezzati, Alberto, Berry, Claire, Bouchara, Jean-Philippe, Brokaar, Edwin, Brown, Whitney, Azevedo, Pilar, Durieu, Isabelle et al (show 34 more authors) , Ekkelenkamp, Miquel, Finlayson, Felicity, Forton, Julian, Gardecki, Johanna, Hodkova, Pavla, Hong, Gina, Lowdon, Jacqueline, Madge, Su, Martin, Clémence, McKone, Edward, Munck, Anne, Ooi, Chee Y, Perrem, Lucy, Piper, Amanda, Prayle, Andrew, Ratjen, Felix, Rosenfeld, Margaret, Sanders, Don B, Schwarz, Carsten, Taccetti, Giovanni, Wainwright, Claire, West, Natalie E, Wilschanski, Michael, Bevan, Amanda, Castellani, Carlo, Drevinek, Pavel, Gartner, Silvia, Gramegna, Andrea, Lammertyn, Elise, Landau, Eddie Edwina C, Plant, Barry J, Smyth, Alan R, van Koningsbruggen-Rietschel, Silke and Middleton, Peter G (2024) Standards for the care of people with cystic fibrosis (CF); recognising and addressing CF health issues. Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society. S1569-1993(24)00005-5-S1569-1993(24)00005-5.

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Southern, Kevin W ORCID: 0000-0001-6516-9083, Castellani, Carlo, Lammertyn, Elise, Smyth, Alan, VanDevanter, Donald, van Koningsbruggen-Rietschel, Silke, Barben, Juerg, Bevan, Amanda, Brokaar, Edwin, Collins, Sarah et al (show 32 more authors) , Connett, Gary J, Daniels, Thomas WV, Davies, Jane, Declercq, Dimitri, Gartner, Silvia, Gramegna, Andrea, Hamilton, Naomi, Hauser, Jenny, Kashirskaya, Nataliya, Kessler, Laurence, Lowdon, Jacqueline, Makukh, Halyna, Martin, Clemence, Morrison, Lisa, Nazareth, Dilip ORCID: 0000-0002-6114-0467, Noordhoek, Jacquelien, O'Neill, Ciaran, Owen, Elizabeth, Oxley, Helen, Raraigh, Karen S, Raynal, Caroline, Robinson, Karen, Roehmel, Jobst, Schwarz, Carsten, Sermet, Isabelle, Shteinberg, Michal, Sinha, Ian, Takawira, Constance, van Mourik, Peter, Verkleij, Marieke, Waller, Michael D and Duff, Alistair (2023) Standards of care for <i>CFTR</i> variant-specific therapy (including modulators) for people with cystic fibrosi. JOURNAL OF CYSTIC FIBROSIS, 22 (1). pp. 17-30.

Murphy, J ORCID: 0000-0003-4656-3004 (2019) Systematic evaluation of F508del variant specific therapies for people with cystic fibrosis. Master of Philosophy thesis, University of Liverpool.

Lee, Tim WR, Southern, Kevin W ORCID: 0000-0001-6516-9083, Perry, Luke A, Penny-Dimri, Jahan C and Aslam, Aisha A (2016) Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung disease. COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 2016 (6). CD005599-.

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Moore, Matthew P, Lamont, Iain L, Williams, David, Paterson, Steve ORCID: 0000-0002-1307-2981, Kukavica-Ibrulj, Irena, Tucker, Nicholas P, Kenna, Dervla TD, Turton, Jane F, Jeukens, Julie, Freschi, Luca et al (show 10 more authors) , Wee, Bryan A, Loman, Nicholas J, Holden, Stephen, Manzoor, Susan, Hawkey, Peter, Southern, Kevin W ORCID: 0000-0001-6516-9083, Walshaw, Martin J, Levesque, Roger C, Fothergill, Joanne L ORCID: 0000-0002-7012-1508 and Winstanley, Craig ORCID: 0000-0002-2662-8053 (2021) Transmission, adaptation and geographical spread of the<i> Pseudomonas</i><i> aeruginosa</i> Liverpool epidemic strain. MICROBIAL GENOMICS, 7 (3). mgen000511-.

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Barben, Jurg, Castellani, Carlo, Munck, Anne, Davies, Jane C, De Winter-de Groot, Karin M, Gartner, Silvia, Kashirskaya, Nataliya, Linnane, Barry, Mayell, Sarah J, McColley, Susanna et al (show 8 more authors) , Ooi, Chee Y, Proesmans, Marijke, Ren, Clement L, Salinas, Danieli, Sands, Dorota, Sermet-Gaudelus, Isabelle, Sommerburg, Olaf and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2021) Updated guidance on the management of children with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID). JOURNAL OF CYSTIC FIBROSIS, 20 (5). pp. 810-819.

Barben, Jürg and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2020) Why Do We Screen Newborn Infants for Cystic Fibrosis? International journal of neonatal screening, 6 (3). 56-.

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Barben, Jurg, Castellani, Carlo, Dankert-Roelse, Jeannette, Gartner, Silvia, Kashirskaya, Nataliya, Linnane, Barry, Mayell, Sarah, Munck, Anne, Sands, Dorota, Sommerburg, Olaf et al (show 3 more authors) , Pybus, Simon, Winters, Victoria and Southern, Kevin W ORCID: 0000-0001-6516-9083 (2017) The expansion and performance of national newborn screening programmes for cystic fibrosis in Europe. JOURNAL OF CYSTIC FIBROSIS, 16 (2). pp. 207-213.

Shelley, James, Fairclough, Stuart J, Knowles, Zoe R, Southern, Kevin W ORCID: 0000-0001-6516-9083, McCormack, Pamela, Dawson, Ellen A, Graves, Lee EF and Hanlon, Claire (2018) A formative study exploring perceptions of physical activity and physical activity monitoring among children and young people with cystic fibrosis and health care professionals. BMC PEDIATRICS, 18 (1). 335-.

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Bell, Scott C, Mall, Marcus A, Gutierrez, Hector, Macek, Milan, Madge, Susan, Davies, Jane C, Burgel, Pierre-Regis, Tullis, Elizabeth, Castaos, Claudio, Castellani, Carlo et al (show 28 more authors) , Byrnes, Catherine A, Cathcart, Fiona, Chotirmall, Sanjay H, Cosgriff, Rebecca, Eichler, Irmgard, Fajac, Isabelle, Goss, Christopher H, Drevinek, Pavel, Farrell, Philip M, Gravelle, Anna M, Havermans, Trudy, Mayer-Hamblett, Nicole, Kashirskaya, Nataliya, Kerem, Eitan, Mathew, Joseph L, McKone, Edward F, Naehrlich, Lutz, Nasr, Samya Z, Oates, Gabriela R, O'Neill, Ciaran, Pypops, Ulrike, Raraigh, Karen S, Rowe, Steven M, Southern, Kevin W ORCID: 0000-0001-6516-9083, Sivam, Sheila, Stephenson, Anne L, Zampoli, Marco and Ratjen, Felix (2020) The future of cystic fibrosis care: a global perspective. LANCET RESPIRATORY MEDICINE, 8 (1). pp. 65-124.

Foil, Kimberly E, Powers, Amy, Raraigh, Karen S, Wallis, Kimberly, Southern, Kevin W ORCID: 0000-0001-6516-9083 and Salinas, Danieli (2019) The increasing challenge of genetic counseling for cystic fibrosis. JOURNAL OF CYSTIC FIBROSIS, 18 (2). pp. 167-174.

Rouse, Claudia, Mistry, Punam, Rayner, Oli, Nickless, Jess, Wan, Mandy, Southern, Kevin W ORCID: 0000-0001-6516-9083 and Batchelor, Hannah K (2017) A mixed methods study of the administration of flucloxacillin oral liquid; identifying strategies to overcome administration issues of medicines with poor palatability. INTERNATIONAL JOURNAL OF PHARMACY PRACTICE, 25 (5). pp. 326-334.

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Rosenfeld, Margaret, Cunningham, Steve, Harris, William T, Lapey, Allen, Regelmann, Warren E, Sawicki, Gregory S, Southern, Kevin W ORCID: 0000-0001-6516-9083, Chilvers, Mark, Higgins, Mark, Tian, Simon et al (show 2 more authors) , Cooke, Jon and Davies, Jane C (2019) An open-label extension study of ivacaftor in children with CF and a <i>CFTR</i> gating mutation initiating treatment at age 2-5 years (KLIMB). JOURNAL OF CYSTIC FIBROSIS, 18 (6). pp. 838-843.

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Terlizzi, Vito, Claut, Laura, Tosco, Antonella, Colombo, Carla, Raia, Valeria, Fabrizzi, Benedetta, Lucarelli, Marco, Angeloni, Antonio, Cimino, Giuseppe, Castaldo, Alice et al (show 11 more authors) , Marsiglio, Laura, Timpano, Silviana, Cirilli, Natalia, Moroni, Laura, Festini, Filippo, Piccinini, Pietro, Zavataro, Lucia, Bonomi, Paolo, Taccetti, Giovanni, Southern, Kevin W ORCID: 0000-0001-6516-9083 and Padoan, Rita (2021) A survey of the prevalence, management and outcome of infants with an inconclusive diagnosis following newborn bloodspot screening for cystic fibrosis (CRMS/CFSPID) in six Italian centres. JOURNAL OF CYSTIC FIBROSIS, 20 (5). pp. 828-834.